Respiratory function results
| Patient | Respiratory function (most recent) | Prebronchodilator FVC decline (mL/year) | Prebronchodilator FEV1 decline (mL/year) | Duration of follow-up (months) |
| 1 | Normal spirometry, reduced gas transfer (DLCO 67%) | 750 | 450 | 8 |
| 2 | Restrictive defect (FVC 49%), reduced gas transfer (DLCO 41%) | 994 | 788 | 14 |
| 3 | Mixed obstructive/restrictive defect (FEV1 47%, FVC 55%), reduced gas transfer (DLCO 53%) | 260 | 250 | 47 |
| 4 | Mixed obstructive/restrictive defect (FEV1 20%, FVC 60%), reduced gas transfer (DLCO 26%) | 180 | 246 | 35 |
| 5 | Restrictive defect (FVC 62%), reduced gas transfer (DLCO 65%) | 333 | 413 | 18 |
| 6 | Mixed obstructive/restrictive defect (FEV1 53%, FVC 71%) | Not available | Not available | 0 |
| 7 | Restrictive defect (FVC 54%), reduced gas transfer (DLCO 31%) | 171 | 171 | 7 |
Patient 6 longitudinal results not available for evaluation.
DLCO, diffusing capacity of the lungs for carbon monoxide; FEV1, forced expiratory volume in 1 s; FVC, forced vital capacity.