Results of lung function and exercise tests (n=38)
| Parameters | Mean (SD) |
|---|---|
| FEV1, % pred | 81.8 (19.6) |
| FVC, % pred | 79.8 (19.4) |
| FEV1/FVC ratio, % | 73.0 (9.6) |
| TLC, % pred | 80.4 (20.5) |
| DLCO, % pred | 71.0 (22.9) |
| VO2max, % pred | 68.8 (20.6) |
| Desaturation, % | 2.6 (3.1) |
| Max. heart rate, % pred | 88.3 (12.1) |
| Vd/Vt at VO2max | 0.22 (0.06) |
| Ve1.0, l/min | 35.7 (10.8) |
| Ve50%, l/min | 44.2 (13.4) |
| Resting PaO2, mmHg | 82.7 (10.7) |
| A-a gradient, mmHg | 17.7 (11.4) |
| Symptom scores | 1.1 (1.5) |
| Body mass index, kg/m2 | 27.2 (3.6) |